Hepatocellular carcinoma and solid pseudopapillary neoplasm of the pancreas complicating familial adenomatous polyposis: two cases and review of the literature
Abstract Familial adenomatous polyposis (FAP) is characterized by colorectal polyposis and extracolonic tumors. Adenocarcinoma of the pancreas and hepatocellular carcinoma are rare in FAP. In this case series, we describe a mother and daughter with FAP who developed a hepatocellular carcinoma and solid pseudopapillary neoplasm of the pancreas, respectively..
Medienart: |
E-Artikel |
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Erscheinungsjahr: |
2022 |
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Erschienen: |
2022 |
Enthalten in: |
Zur Gesamtaufnahme - volume:22 |
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Enthalten in: |
Familial cancer - 22(2022), 1 vom: 28. Juli, Seite 77-82 |
Sprache: |
Englisch |
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Beteiligte Personen: |
El Halabi, Jessica [VerfasserIn] |
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Links: |
Volltext [lizenzpflichtig] |
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BKL: | |
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Themen: |
Familial adenomatosous polyposis |
Anmerkungen: |
© The Author(s), under exclusive licence to Springer Nature B.V. 2022 |
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doi: |
10.1007/s10689-022-00305-0 |
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funding: |
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Förderinstitution / Projekttitel: |
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PPN (Katalog-ID): |
OLC2133296670 |
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520 | |a Abstract Familial adenomatous polyposis (FAP) is characterized by colorectal polyposis and extracolonic tumors. Adenocarcinoma of the pancreas and hepatocellular carcinoma are rare in FAP. In this case series, we describe a mother and daughter with FAP who developed a hepatocellular carcinoma and solid pseudopapillary neoplasm of the pancreas, respectively. | ||
650 | 4 | |a Familial adenomatosous polyposis | |
650 | 4 | |a Hepatocellular carcinoma | |
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700 | 1 | |a Liska, David |4 aut | |
700 | 1 | |a Burke, Carol A. |4 aut | |
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