A Rare but Fatal Behçet Variant : The Hughes-Stovin Syndrome-Successful Case Report and New Evidence from Literature Review
The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/)..
Hughes-Stovin syndrome (HSS) is a rare potentially fatal vasculitis supposedly belonging to the spectrum of Behçet disease without ocular involvement. HSS tends to play by a temporal pattern, starting with thrombosis and followed by formation of pulmonary aneurysms. Since its mortality can reach 25% of cases, early recognition and appropriate therapy represent the major clinical challenges. We describe a rare case of HSS successfully treated via multidisciplinary management by an endovascular approach and immunosuppressive therapy.
| Medienart: |
E-Artikel |
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| Erscheinungsjahr: |
2023 |
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| Erschienen: |
2023 |
| Enthalten in: |
Zur Gesamtaufnahme - volume:11 |
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| Enthalten in: |
Aorta (Stamford, Conn.) - 11(2023), 4 vom: 26. Aug., Seite 156-161 |
| Sprache: |
Englisch |
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| Beteiligte Personen: |
Ascoli Marchetti, Andrea [VerfasserIn] |
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| Anmerkungen: |
Date Revised 26.04.2024 published: Print-Electronic Citation Status PubMed-not-MEDLINE |
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| doi: |
10.1055/s-0043-1777994 |
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| funding: |
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| Förderinstitution / Projekttitel: |
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| PPN (Katalog-ID): |
NLM370209338 |
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| 520 | |a The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/). | ||
| 520 | |a Hughes-Stovin syndrome (HSS) is a rare potentially fatal vasculitis supposedly belonging to the spectrum of Behçet disease without ocular involvement. HSS tends to play by a temporal pattern, starting with thrombosis and followed by formation of pulmonary aneurysms. Since its mortality can reach 25% of cases, early recognition and appropriate therapy represent the major clinical challenges. We describe a rare case of HSS successfully treated via multidisciplinary management by an endovascular approach and immunosuppressive therapy | ||
| 650 | 4 | |a Journal Article | |
| 700 | 1 | |a Belvivere, Lorella |e verfasserin |4 aut | |
| 700 | 1 | |a Argirò, Renato |e verfasserin |4 aut | |
| 700 | 1 | |a Kroegler, Barbara |e verfasserin |4 aut | |
| 700 | 1 | |a Oddi, Fabio M |e verfasserin |4 aut | |
| 700 | 1 | |a Pennetta, Federico |e verfasserin |4 aut | |
| 700 | 1 | |a Giorgi, Alice de |e verfasserin |4 aut | |
| 700 | 1 | |a Fazzini, Stefano |e verfasserin |4 aut | |
| 700 | 1 | |a Morosetti, Daniele |e verfasserin |4 aut | |
| 700 | 1 | |a Triggianese, Paola |e verfasserin |4 aut | |
| 700 | 1 | |a Greco, Elisabetta |e verfasserin |4 aut | |
| 700 | 1 | |a D'Antonio, Arianna |e verfasserin |4 aut | |
| 700 | 1 | |a Coccia, Ilaria |e verfasserin |4 aut | |
| 700 | 1 | |a Tesauro, Manfredi |e verfasserin |4 aut | |
| 700 | 1 | |a Sangiuolo, Federica |e verfasserin |4 aut | |
| 700 | 1 | |a Ippoliti, Arnaldo |e verfasserin |4 aut | |
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