S2k guidelines on diagnosis and treatment of linear IgA dermatosis initiated by the European Academy of Dermatology and Venereology

© 2024 The Authors. Journal of the European Academy of Dermatology and Venereology published by John Wiley & Sons Ltd on behalf of European Academy of Dermatology and Venereology..

INTRODUCTION: Linear IgA dermatosis (LAD) is a rare subepidermal autoimmune bullous disease (AIBD) defined by predominant or exclusive immune deposits of immunoglobulin A at the basement membrane zone of skin or mucous membranes. This disorder is a rare, clinically and immunologically heterogeneous disease occurring both in children and in adults. The aim of this project is to present the main clinical features of LAD, to propose a diagnostic algorithm and provide management guidelines based primarily on experts' opinion because of the lack of large methodologically sound clinical studies.

METHODS: These guidelines were initiated by the European Academy of Dermatology and Venereology (EADV) Task Force Autoimmune Bullous Diseases (AIBD). To achieve a broad consensus for these S2k consensus-based guidelines, a total of 29 experts from different countries, both European and non-European, including dermatologists, paediatric dermatologists and paediatricians were invited. All members of the guidelines committee agreed to develop consensus-based (S2k) guidelines. Prior to a first virtual consensus meeting, each of the invited authors elaborated a section of the present guidelines focusing on a selected topic, based on the relevant literature. All drafts were circulated among members of the writing group, and recommendations were discussed and voted during two hybrid consensus meetings.

RESULTS: The guidelines summarizes evidence-based and expert opinion-based recommendations (S2 level) on the diagnosis and treatment of LAD.

CONCLUSION: These guidelines will support dermatologists to improve their knowledge on the diagnosis and management of LAD.

Medienart:

E-Artikel

Erscheinungsjahr:

2024

Erschienen:

2024

Enthalten in:

Zur Gesamtaufnahme - year:2024

Enthalten in:

Journal of the European Academy of Dermatology and Venereology : JEADV - (2024) vom: 29. Feb.

Sprache:

Englisch

Beteiligte Personen:

Caux, Frédéric [VerfasserIn]
Patsatsi, Aikaterini [VerfasserIn]
Karakioulaki, Meropi [VerfasserIn]
Antiga, Emiliano [VerfasserIn]
Baselga, Eulalia [VerfasserIn]
Borradori, Luca [VerfasserIn]
Caproni, Marzia [VerfasserIn]
Cardones, Adela R [VerfasserIn]
Chandran, Nisha Suyien [VerfasserIn]
Dräger, Sören [VerfasserIn]
Drenovska, Kossara [VerfasserIn]
Goebeler, Matthias [VerfasserIn]
Günther, Claudia [VerfasserIn]
Hofmann, Silke C [VerfasserIn]
Ioannides, Dimitrios [VerfasserIn]
Joly, Pascal [VerfasserIn]
Marinović, Branka [VerfasserIn]
Mariotti, Elena Biancamaria [VerfasserIn]
Marzano, Angelo Valerio [VerfasserIn]
Morel, Kimberly D [VerfasserIn]
Murrell, Dedee F [VerfasserIn]
Prost, Catherine [VerfasserIn]
Sárdy, Miklós [VerfasserIn]
Setterfield, Jane [VerfasserIn]
Skiljevic, Dusan [VerfasserIn]
Uzun, Soner [VerfasserIn]
Vassileva, Snejina [VerfasserIn]
Zambruno, Giovanna [VerfasserIn]
Schmidt, Enno [VerfasserIn]

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Journal Article

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Date Revised 29.02.2024

published: Print-Electronic

Citation Status Publisher

doi:

10.1111/jdv.19880

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM369109821