Susac's syndrome : a rare autoimmune angiopathy in a 71-year-old patient
BACKGROUND: Susac's syndrome is an autoimmune angiopathy classically leading to the triad of encephalopathy, retinopathy and hearing loss. Multidisciplinarity is essential for diagnosis, which means in more detail a MRI-cerebrum, fluorescence angiography (FAG) and audiography. Early treatment is key since it is associated with better prognosis and reversibility.
CASE DESCRIPTION: This article presents a 71-year-old woman with multiple episodes of separate complaints (aphasia, behavioral changes, amnesia and vertigo with tinnitus). The MRI-cerebrum suspected Susac's syndrome with typical callosal lesions. An abnormal FAG and audiography completed the diagnostic triad of Susac's syndrome. Thereafter, treatment with immunosuppressants was initiated, which resulted in cognitive improvement.
| Medienart: |
E-Artikel |
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| Erscheinungsjahr: |
2024 |
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| Erschienen: |
2024 |
| Enthalten in: |
Zur Gesamtaufnahme - volume:168 |
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| Enthalten in: |
Nederlands tijdschrift voor geneeskunde - 168(2024) vom: 16. Jan. |
| Sprache: |
Niederländisch |
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| Weiterer Titel: |
Syndroom van Susac |
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| Beteiligte Personen: |
Teunissen, Esther M M [VerfasserIn] |
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| Themen: |
Case Reports |
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| Anmerkungen: |
Date Completed 07.02.2024 Date Revised 19.03.2024 published: Electronic Citation Status MEDLINE |
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| Förderinstitution / Projekttitel: |
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| PPN (Katalog-ID): |
NLM368085775 |
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| 520 | |a BACKGROUND: Susac's syndrome is an autoimmune angiopathy classically leading to the triad of encephalopathy, retinopathy and hearing loss. Multidisciplinarity is essential for diagnosis, which means in more detail a MRI-cerebrum, fluorescence angiography (FAG) and audiography. Early treatment is key since it is associated with better prognosis and reversibility | ||
| 520 | |a CASE DESCRIPTION: This article presents a 71-year-old woman with multiple episodes of separate complaints (aphasia, behavioral changes, amnesia and vertigo with tinnitus). The MRI-cerebrum suspected Susac's syndrome with typical callosal lesions. An abnormal FAG and audiography completed the diagnostic triad of Susac's syndrome. Thereafter, treatment with immunosuppressants was initiated, which resulted in cognitive improvement | ||
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