Isolated embryonal rhabdomyosarcoma of the anterior petrous bone in a young child : Focusing on the intra-operative diagnosis and differentials
OBJECTIVE: Rhabdomyosarcoma is a common soft tissue tumor, but isolated involvement of anterior portion of petrous bone is exceedingly rare. Here, we present a case of embryonal rhabdomyosarcoma involving the anterior petrous without involvement of the mastoid and middle ear.
PATIENT: A 6-year-old boy presented with a progressive right side lower motor neuron facial paresis for 1-month duration along with headache and recurrent vomiting episodes. Radiology showed a contrast-enhancing lesion involving the right petrous apex. He underwent craniotomy and excision of the lesion. Based on the frozen section, a diagnosis of rhabdomyosarcoma was rendered, and gross total resection could be achieved. Postoperative course was uneventful.
CONCLUSION: Isolated petrous bone involvement of embryonal rhabdomyosarcoma is a rare presentation. Intra-operative frozen section plays a key role in decision making regarding the extent of excision. Hence, a prompt and accurate diagnosis is essential in managing these cases.
| Medienart: |
E-Artikel |
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| Erscheinungsjahr: |
2024 |
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| Erschienen: |
2024 |
| Enthalten in: |
Zur Gesamtaufnahme - volume:43 |
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| Enthalten in: |
Clinical neuropathology - 43(2024), 2 vom: 12. März, Seite 48-52 |
| Sprache: |
Englisch |
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| Beteiligte Personen: |
Panda, Ipsita [VerfasserIn] |
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| Anmerkungen: |
Date Completed 11.04.2024 Date Revised 11.04.2024 published: Print Citation Status MEDLINE |
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| doi: |
10.5414/NP301586 |
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| funding: |
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| Förderinstitution / Projekttitel: |
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NLM365758515 |
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| 245 | 1 | 0 | |a Isolated embryonal rhabdomyosarcoma of the anterior petrous bone in a young child |b Focusing on the intra-operative diagnosis and differentials |
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| 520 | |a OBJECTIVE: Rhabdomyosarcoma is a common soft tissue tumor, but isolated involvement of anterior portion of petrous bone is exceedingly rare. Here, we present a case of embryonal rhabdomyosarcoma involving the anterior petrous without involvement of the mastoid and middle ear | ||
| 520 | |a PATIENT: A 6-year-old boy presented with a progressive right side lower motor neuron facial paresis for 1-month duration along with headache and recurrent vomiting episodes. Radiology showed a contrast-enhancing lesion involving the right petrous apex. He underwent craniotomy and excision of the lesion. Based on the frozen section, a diagnosis of rhabdomyosarcoma was rendered, and gross total resection could be achieved. Postoperative course was uneventful | ||
| 520 | |a CONCLUSION: Isolated petrous bone involvement of embryonal rhabdomyosarcoma is a rare presentation. Intra-operative frozen section plays a key role in decision making regarding the extent of excision. Hence, a prompt and accurate diagnosis is essential in managing these cases | ||
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| 700 | 1 | |a Salunke, Pravin |e verfasserin |4 aut | |
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