An extreme case of cor triatriatum mimicking hypoplastic left heart syndrome and combined pulmonary vein stenosis

A 65-day-old girl presented to the emergency room with lethargy, requiring emergency venoarterial extracorporeal membrane oxygenation for refractory cardiogenic shock. Initially, hypoplastic left heart syndrome was suspected. However, cor triatriatum with a pinpoint opening on the membrane was diagnosed based on a detailed echocardiographic examination. After membrane resection, the left heart size was restored. However, follow-up echocardiography performed 4 months later showed occlusion of both upper pulmonary veins and stenosis in both lower pulmonary veins. Hybrid balloon angioplasty was performed in all pulmonary veins, and stents were inserted into the right upper and lower pulmonary veins. Despite repeated balloon angioplasty, all pulmonary vein stenosis progressed over 6 months and the patient expired while waiting for a heart-lung transplant. Even after successful repair of cor triatriatum, short-term close follow-up is required for detecting the development of pulmonary vein stenosis.

Medienart:

E-Artikel

Erscheinungsjahr:

2024

Erschienen:

2024

Enthalten in:

Zur Gesamtaufnahme - volume:34

Enthalten in:

Cardiology in the young - 34(2024), 1 vom: 28. Jan., Seite 205-208

Sprache:

Englisch

Beteiligte Personen:

Hong, Hee Ju [VerfasserIn]
Kwon, Hye Won [VerfasserIn]
Kwak, Jae Gun [VerfasserIn]
Lee, Sang Yun [VerfasserIn]
Lee, Yoon Seong [VerfasserIn]

Links:

Volltext

Themen:

Angioplasty
Balloon
Case Reports
Cor triatriatum
Journal Article
Pulmonary vein stenosis

Anmerkungen:

Date Completed 29.01.2024

Date Revised 29.01.2024

published: Print-Electronic

Citation Status MEDLINE

doi:

10.1017/S1047951123003724

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM365093203