Speech reception after cochlear implantation for Cogan's syndrome : Case series following CARE guidelines

Copyright © 2023 Elsevier Masson SAS. All rights reserved..

INTRODUCTION: Cogan's syndrome is a rare form of vasculitis mainly affecting young subjects of whatever gender, associating cochleovestibular and ophthalmological damage. Despite medical treatment, auditory prognosis is uncertain, with 50-60% of patients showing irreversible severe to profound hearing loss, thus being candidates for cochlear implantation. Following CARE guidelines, we report 10 cases of cochlear implantation in Cogan's syndrome, with assessment of speech reception threshold and maximum intelligibility after a minimum 1 year's experience with the implant.

CASE SERIES: Ten patients from 4 centers received cochlear implants (14 implants) for Cogan's syndrome between 2005 and 2020. After 1 year's experience, there was significant improvement in speech reception threshold (P=0.0002) and maximum intelligibility (P=0.0002).

CONCLUSION-DISCUSSION: Audiovestibular signs associated with ophthalmological manifestations should suggest Cogan's syndrome. Hearing impairment is usually irreversible. Cochlear implantation may be necessary and improves hearing performance.

Medienart:

E-Artikel

Erscheinungsjahr:

2023

Erschienen:

2023

Enthalten in:

Zur Gesamtaufnahme - volume:140

Enthalten in:

European annals of otorhinolaryngology, head and neck diseases - 140(2023), 5 vom: 19. Sept., Seite 235-238

Sprache:

Englisch

Beteiligte Personen:

Boumghit, Y [VerfasserIn]
Boucher, S [VerfasserIn]
Godey, B [VerfasserIn]
Michel, G [VerfasserIn]
Bakhos, D [VerfasserIn]

Links:

Volltext

Themen:

Case series
Cochlear implantation
Cogan
Hearing
Journal Article
Vestibular

Anmerkungen:

Date Completed 02.10.2023

Date Revised 02.10.2023

published: Print-Electronic

Citation Status MEDLINE

doi:

10.1016/j.anorl.2023.06.005

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM359798632