A young woman with auto-immune pancreatitis

BACKGROUND: Acute pancreatitis is a frequently diagnosed disease. The majority is caused by cholelithiasis or alcohol. There are also two forms of auto-immune pancreatitis (AIP). Type 2 AIP presents on a younger age compared with IgG4 related pancreatitis. Clinical presentation as an acute pancreatitis, a mass in the pancreas or with jaundice. There is an association with inflammatory bowel disease.

CASE DESCRIPTION: A young patient with Crohn's disease developed abdominal pain compatible with acute pancreatitis. After exclusion of other etiologies a diagnosis of type 2 auto-immune pancreatitis was made with MRI/MRCP and typical histology. She was clinically successfully treated with steroids and follow up scan clearly showed improvement. Steroids were slowly withdrawn.

CONCLUSION: Also young patients and patients with a normal IgG4 can have an AIP. Diagnosis is based on clinical, radiological and histological criteria. Type 2 AIP is treated with steroids without the need for maintenance therapy.

Medienart:

E-Artikel

Erscheinungsjahr:

2023

Erschienen:

2023

Enthalten in:

Zur Gesamtaufnahme - volume:167

Enthalten in:

Nederlands tijdschrift voor geneeskunde - 167(2023) vom: 16. März

Sprache:

Niederländisch

Weiterer Titel:

Acute pancreatitis bij een jonge patiënt

Beteiligte Personen:

Zoutendijk, Roeland [VerfasserIn]
van Santvoort, Hjalmar C [VerfasserIn]
Raicu, Mihaela G [VerfasserIn]
Bollen, Thomas L [VerfasserIn]
Verdonk, Robert C [VerfasserIn]

Themen:

Case Reports
English Abstract
Immunoglobulin G
Journal Article
Steroids

Anmerkungen:

Date Completed 21.03.2023

Date Revised 17.04.2023

published: Electronic

Citation Status MEDLINE

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM354343629