Acute Abdomen and Adrenal Swelling as the First Manifestations of TAFRO Syndrome

TAFRO syndrome, a rare systemic inflammatory disorder, commonly develops in an acute or subacute manner, with an aggressive clinical behavior. A substantial number of cases of TAFRO syndrome presenting with abdominal pain, and adrenal abnormalities on imaging have also been reported. A 54-year-old man developed severe acute abdominal pain. Bilateral adrenal swelling was detected on computed tomography. Although the abdominal pain resolved spontaneously, a fever and anasarca were observed. The patient was eventually diagnosed with TAFRO syndrome, and corticosteroid administration resulted in remission. TAFRO syndrome should be included in the differential diagnosis of acute abdomen and adrenal abnormalities.

Medienart:

E-Artikel

Erscheinungsjahr:

2023

Erschienen:

2023

Enthalten in:

Zur Gesamtaufnahme - volume:62

Enthalten in:

Internal medicine (Tokyo, Japan) - 62(2023), 11 vom: 01. Juni, Seite 1675-1681

Sprache:

Englisch

Beteiligte Personen:

Fujimi, Akihito [VerfasserIn]
Nagamachi, Yasuhiro [VerfasserIn]
Yamauchi, Naofumi [VerfasserIn]
Onoyama, Naoki [VerfasserIn]
Matsuno, Teppei [VerfasserIn]
Miyajima, Naoya [VerfasserIn]
Koike, Kazuhiko [VerfasserIn]
Goto, Yoshiro [VerfasserIn]
Ihara, Kohji [VerfasserIn]
Nishisato, Takuji [VerfasserIn]
Kobune, Masayoshi [VerfasserIn]

Links:

Volltext

Themen:

Acute abdomen
Adrenal Cortex Hormones
Adrenal abnormality
Case Reports
Corticosteroids
Journal Article
TAFRO syndrome

Anmerkungen:

Date Completed 02.06.2023

Date Revised 01.07.2023

published: Print-Electronic

Citation Status MEDLINE

doi:

10.2169/internalmedicine.0267-22

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM345880676