Imaging of eosinophilic fasciitis in ultrasound and MRI (magnetic resonance imaging) : a case report

© 2022. The Author(s)..

Eosinophilic fasciitis (EF, also known as Shulman syndrome) is an uncommon connective tissue disease characterized by inflammatory thickening of the fasciae as well as swelling and hardening of the skin. It mostly affects the lower extremities. Swollen and indurated skin, together with the groove sign, are typical clinical signs. So far, biopsy evidence of inflammation and thickening of the fascia has been the gold standard for diagnosis. Magnetic resonance imaging (MRI) is mentioned in the literature as an alternative method for confirming the diagnosis. We present a case of asymmetric EF in a 54-year-old German male. He came with painful induration of the right forearm, with a characteristic groove sign and limitation of motion of the right hand. The blood count revealed eosinophilia with 0.57 G/l or 9.6% (normal: 0.05-0.5 G/l and 0.5-5.5%), ANA and ENA were negative. The diagnosis was confirmed histologically and we were able to detect a thickened fascia in MRI and ultrasound imaging. The EF also appeared in the left lateral malleolus during the course of the illness. Treatment was carried out with prednisolone and methotrexate.

Medienart:

E-Artikel

Erscheinungsjahr:

2024

Erschienen:

2024

Enthalten in:

Zur Gesamtaufnahme - volume:83

Enthalten in:

Zeitschrift fur Rheumatologie - 83(2024), 2 vom: 18. März, Seite 134-138

Sprache:

Deutsch

Weiterer Titel:

Darstellung der eosinophilen Fasziitis in Ultraschall und MRT (Magnetresonanztomographie): ein Fallbericht

Beteiligte Personen:

Gerritzen, Nicolas [VerfasserIn]
Ziob, Jana [VerfasserIn]
Brossart, Peter [VerfasserIn]
Schäfer, Valentin S [VerfasserIn]

Links:

Volltext

Themen:

Case Reports
English Abstract
Eosinophilia
Groove sign
Journal Article
Shulman syndrome
Sonography
Thickening of the fascia

Anmerkungen:

Date Completed 29.02.2024

Date Revised 02.03.2024

published: Print-Electronic

Citation Status MEDLINE

doi:

10.1007/s00393-022-01207-3

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM340986808