Polysplenia syndrome and sickle cell trait : extensive deep venous thrombosis from venous stasis and hypercoagulability

Copyright © 2021 Elsevier Inc. All rights reserved..

Deep venous thrombosis is a hitherto under-recognized complication occurring in patients with polysplenia syndrome, despite the high prevalence of venous anomalies such as interrupted inferior vena cava (IVC) with azygos/hemiazygos continuation. Here we report the first case of concurrent polysplenia (as evidenced by interrupted IVC with azygos/hemiazygos continuation, multiple left-sided spleens, bowel malrotation with inverted mesenteric veins, preduodenal portal vein, and pancreatic hypoplasia/partial agenesis of the dorsal pancreas) and sickle cell trait, complicated by extensive deep venous thrombosis refractory to medical and interventional radiologic management.

Medienart:

E-Artikel

Erscheinungsjahr:

2022

Erschienen:

2022

Enthalten in:

Zur Gesamtaufnahme - volume:82

Enthalten in:

Clinical imaging - 82(2022) vom: 01. Feb., Seite 127-131

Sprache:

Englisch

Beteiligte Personen:

Shahrouki, Puja [VerfasserIn]
Lee, Edward Wolfgang [VerfasserIn]
Ruehm, Stefan [VerfasserIn]

Links:

Volltext

Themen:

Case Reports
Deep venous thrombosis
Heterotaxy
Hypercoagulability
Isomerism
Polysplenia
Sickle cell trait

Anmerkungen:

Date Completed 11.01.2022

Date Revised 31.05.2022

published: Print-Electronic

Citation Status MEDLINE

doi:

10.1016/j.clinimag.2021.11.017

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM333512340