Diagnosis and Management of Fibrotic Interstitial Lung Diseases

Copyright © 2021 Elsevier Inc. All rights reserved..

Nonidiopathic pulmonary fibrosis (non-IPF) progressive fibrotic interstitial lung diseases (PF-ILDs) are a heterogeneous group of ILDs, often challenging to diagnose, although an accurate diagnosis has significant implications for both treatment and prognosis. A subgroup of these patients experiences progressive deterioration in lung function, physical performance, and quality of life after conventional therapy. Risk factors for ILD progression include older age, lower baseline pulmonary function, and a usual interstitial pneumonia pattern. Management of non-IPF P-ILD is both pharmacologic and nonpharmacologic. Antifibrotic drugs, originally approved for IPF, have been considered in patients with other fibrotic ILD subtypes, with favorable results in clinical trials.

Medienart:

E-Artikel

Erscheinungsjahr:

2021

Erschienen:

2021

Enthalten in:

Zur Gesamtaufnahme - volume:42

Enthalten in:

Clinics in chest medicine - 42(2021), 2 vom: 26. Juni, Seite 321-335

Sprache:

Englisch

Beteiligte Personen:

Collins, Bridget F [VerfasserIn]
Luppi, Fabrizio [VerfasserIn]

Links:

Volltext

Themen:

Antifibrotic treatment
Connective tissue disease-interstitial lung disease
Fibrotic hypersensitivity pneumonitis
Idiopathic pulmonary fibrosis
Journal Article
Nintedanib
Pirfenidone
Progressive fibrotic interstitial lung disease
Review
Unclassifiable interstitial lung disease

Anmerkungen:

Date Completed 19.07.2021

Date Revised 19.07.2021

published: Print

Citation Status MEDLINE

doi:

10.1016/j.ccm.2021.03.008

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM325737215