Congenital pulmonary vein stenosis and bronchopulmonary vascular malformation
The objective is demonstrate the diagnostic process and evolution of a patient with a diagnosis of congenital pulmonary vein stenosis and broncho-pulmonary vascular malformation. One year old female patient with repeated bronchopneumonia, acrocyanosis, split S2, cardiomegaly, pulmonary hypertension, with a clinical diagnosis of atrial septal defect. The echocardiogram demonstrated left sided vein pulmonary stenosis. The cardiac catheterization demonstrated arterial-venous fistulas apical on the right lung. Magnetic Resonance image and angiography showed an aberrant arterial vessel parallel to the abdominal aorta which flow the right pulmonary lobe. The cardiac tomography angiography reported confluence of right-sided pulmonary veins. A lobectomy is performed. Patient died in post-operative due to massive pulmonary hemorrhaging. This is the first patient mentioned in written literature with pulmonary vein stenosis associated with pulmonary sequestration, with normal venous connection. Echocardiography represents the specific standard study ideal for initial diagnostic for patients with pulmonary vein stenosis.
| Medienart: |
E-Artikel |
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| Erscheinungsjahr: |
2021 |
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| Erschienen: |
2021 |
| Enthalten in: |
Zur Gesamtaufnahme - volume:91 |
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| Enthalten in: |
Archivos de cardiologia de Mexico - 91(2021), 2 vom: 16. März, Seite 355-360 |
| Sprache: |
Spanisch |
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| Weiterer Titel: |
Estenosis congénita de venas pulmonares y malformación vascular broncopulmonar |
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| Beteiligte Personen: |
De Rubens-Figueroa, Jesús [VerfasserIn] |
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| Links: |
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| Themen: |
Congenital heart disease |
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| Anmerkungen: |
Date Revised 20.10.2023 published: Electronic Citation Status PubMed-not-MEDLINE |
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| doi: |
10.24875/ACM.20000362 |
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| funding: |
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| Förderinstitution / Projekttitel: |
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| PPN (Katalog-ID): |
NLM322823560 |
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| 100 | 1 | |a De Rubens-Figueroa, Jesús |e verfasserin |4 aut | |
| 245 | 1 | 0 | |a Congenital pulmonary vein stenosis and bronchopulmonary vascular malformation |
| 246 | 3 | 3 | |a Estenosis congénita de venas pulmonares y malformación vascular broncopulmonar |
| 264 | 1 | |c 2021 | |
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| 500 | |a Date Revised 20.10.2023 | ||
| 500 | |a published: Electronic | ||
| 500 | |a Citation Status PubMed-not-MEDLINE | ||
| 520 | |a The objective is demonstrate the diagnostic process and evolution of a patient with a diagnosis of congenital pulmonary vein stenosis and broncho-pulmonary vascular malformation. One year old female patient with repeated bronchopneumonia, acrocyanosis, split S2, cardiomegaly, pulmonary hypertension, with a clinical diagnosis of atrial septal defect. The echocardiogram demonstrated left sided vein pulmonary stenosis. The cardiac catheterization demonstrated arterial-venous fistulas apical on the right lung. Magnetic Resonance image and angiography showed an aberrant arterial vessel parallel to the abdominal aorta which flow the right pulmonary lobe. The cardiac tomography angiography reported confluence of right-sided pulmonary veins. A lobectomy is performed. Patient died in post-operative due to massive pulmonary hemorrhaging. This is the first patient mentioned in written literature with pulmonary vein stenosis associated with pulmonary sequestration, with normal venous connection. Echocardiography represents the specific standard study ideal for initial diagnostic for patients with pulmonary vein stenosis | ||
| 650 | 4 | |a English Abstract | |
| 650 | 4 | |a Journal Article | |
| 650 | 4 | |a Pulmonary vein stenosis | |
| 650 | 4 | |a Congenital heart disease | |
| 650 | 4 | |a Pulmonary heart disease | |
| 650 | 4 | |a Pulmonary sequestration | |
| 700 | 1 | |a Bobadilla-Chávez, José J |e verfasserin |4 aut | |
| 700 | 1 | |a Solórzano-Morales, Sara A |e verfasserin |4 aut | |
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