Erdheim-Chester disease diagnosed with right atrium tumors

Erdheim-Chester disease (ECD) is a very rare form of the non-Langerhans histiocytic multisystem disorder. The cardiac involvement is often challenging and is associated with poor prognosis. Transthoracic echocardiography was used to detect right atrium tumors in a 62-year-old man with heart failure who was admitted to our hospital. The circumferential soft tissue sheathing of the aorta (coated aorta) and fat infiltration around the kidneys (hairy kidneys) was seen on a contrast-enhanced computed tomography strongly suspecting ECD imaging. The patient was diagnosed with ECD based on histopathology reports of the surgical resection tumor. The characteristic imaging findings of ECD may contribute to an early and accurate diagnosis.

Medienart:

E-Artikel

Erscheinungsjahr:

2021

Erschienen:

2021

Enthalten in:

Zur Gesamtaufnahme - volume:62

Enthalten in:

Rinsho ketsueki] The Japanese journal of clinical hematology - 62(2021), 2 vom: 01., Seite 91-93

Sprache:

Japanisch

Beteiligte Personen:

Takeda, Satomi [VerfasserIn]
Murata, Shogo [VerfasserIn]
Tane, Misato [VerfasserIn]
Yoshida, Kikuaki [VerfasserIn]
Iwamoto, Ryuta [VerfasserIn]
Warigaya, Kenji [VerfasserIn]
Sakaki, Ayaka [VerfasserIn]
Yokoya, Yuma [VerfasserIn]
Tanaka, Ken [VerfasserIn]
Tochino, Yuichi [VerfasserIn]
Yamashita, Yusuke [VerfasserIn]
Hosoi, Hiroki [VerfasserIn]
Mushino, Toshiki [VerfasserIn]
Nishikawa, Akinori [VerfasserIn]
Tamura, Shinobu [VerfasserIn]
Sonoki, Takashi [VerfasserIn]

Links:

Volltext

Themen:

Case Reports
Coated aorta
Erdheim-Chester disease
Hairy kidneys
Journal Article

Anmerkungen:

Date Completed 10.03.2021

Date Revised 10.03.2021

published: Print

Citation Status MEDLINE

doi:

10.11406/rinketsu.62.91

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM322360110