Echocardiography for the Assessment of Pulmonary Hypertension and Congenital Heart Disease in the Young

While invasive assessment of hemodynamics and testing of acute vasoreactivity in the catheterization laboratory is the gold standard for diagnosing pulmonary hypertension (PH) and pulmonary vascular disease (PVD) in children, transthoracic echocardiography (TTE) serves as the initial diagnostic tool. International guidelines suggest several key echocardiographic variables and indices for the screening studies when PH is suspected. However, due to the complex anatomy and special physiological considerations, these may not apply to patients with congenital heart disease (CHD). Misinterpretation of TTE variables can lead to delayed diagnosis and therapy, with fatal consequences, or-on the other hand-unnecessary invasive diagnostic procedures that have relevant risks, especially in the pediatric age group. We herein provide an overview of the echocardiographic workup of children and adolescents with PH with a special focus on children with CHD, such as ventricular/atrial septal defects, tetralogy of Fallot or univentricular physiology. In addition, we address the use of echocardiography as a tool to assess eligibility for exercise and sports, a major determinant of quality of life and outcome in patients with PH associated with CHD.

Medienart:

E-Artikel

Erscheinungsjahr:

2020

Erschienen:

2020

Enthalten in:

Zur Gesamtaufnahme - volume:11

Enthalten in:

Diagnostics (Basel, Switzerland) - 11(2020), 1 vom: 31. Dez.

Sprache:

Englisch

Beteiligte Personen:

Meinel, Katharina [VerfasserIn]
Koestenberger, Martin [VerfasserIn]
Sallmon, Hannes [VerfasserIn]
Hansmann, Georg [VerfasserIn]
Pieles, Guido E [VerfasserIn]

Links:

Volltext

Themen:

Congenital heart disease
Echocardiography
Exercise assessment
Journal Article
Pulmonary arterial hypertension
Pulmonary hypertension
Review

Anmerkungen:

Date Revised 26.01.2021

published: Electronic

Citation Status PubMed-not-MEDLINE

doi:

10.3390/diagnostics11010049

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM319601641