Primary hemophagocytic lymphohistiocytosis in Iran : report from a single referral center
Hemophagocytic lymphohistiocytosis (HLH) is a rare condition characterized by fever, hepatosplenomegaly, and cytopenia, and widespread accumulation of lymphocytes and histiocytes, sometimes with hemophagocytosis, primarily involving the spleen, lymph nodes, bone marrow, and liver. HLH can either occur sporadically (secondary HLH) or as part of a familial syndrome (primary HLH), including familial HLH and the distinct immunodeficiency syndromes. Herein the authors report 6 Iranian patients with primary HLH and their outcome from a single tertiary-care center.
| Medienart: |
E-Artikel |
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| Erscheinungsjahr: |
2012 |
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| Erschienen: |
2012 |
| Enthalten in: |
Zur Gesamtaufnahme - volume:29 |
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| Enthalten in: |
Pediatric hematology and oncology - 29(2012), 3 vom: 04. Apr., Seite 215-9 |
| Sprache: |
Englisch |
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| Beteiligte Personen: |
Shamsian, Bibi Shahin [VerfasserIn] |
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| Links: |
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| Themen: |
Case Reports |
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| Anmerkungen: |
Date Completed 17.09.2012 Date Revised 16.11.2017 published: Print Citation Status MEDLINE |
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| doi: |
10.3109/08880018.2012.657338 |
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| funding: |
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| Förderinstitution / Projekttitel: |
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| PPN (Katalog-ID): |
NLM216751306 |
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| 520 | |a Hemophagocytic lymphohistiocytosis (HLH) is a rare condition characterized by fever, hepatosplenomegaly, and cytopenia, and widespread accumulation of lymphocytes and histiocytes, sometimes with hemophagocytosis, primarily involving the spleen, lymph nodes, bone marrow, and liver. HLH can either occur sporadically (secondary HLH) or as part of a familial syndrome (primary HLH), including familial HLH and the distinct immunodeficiency syndromes. Herein the authors report 6 Iranian patients with primary HLH and their outcome from a single tertiary-care center | ||
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| 700 | 1 | |a Gharib, Atoosa |e verfasserin |4 aut | |
| 700 | 1 | |a Jadali, Farzaneh |e verfasserin |4 aut | |
| 700 | 1 | |a Arzanian, Mohammad Taghi |e verfasserin |4 aut | |
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