A chylothorax in a young woman: The difficulties of medical management
Abstract Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax is a well‐recognized complication of the condition, management strategies aren't well‐defined, have low success rates and are often only available at tertiary or specialist centres. We describe a case of a young woman referred to pleural clinic with a chylous effusion found to be secondary to lymphangioleiomyomatosis. Initial medical management was unsuccessful and recurrent drainages caused significant complications. Remission was ultimately achieved with a combination of mTOR inhibitors and interventional radiology techniques..
Medienart: |
E-Artikel |
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Erscheinungsjahr: |
2024 |
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Erschienen: |
2024 |
Enthalten in: |
Zur Gesamtaufnahme - volume:12 |
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Enthalten in: |
Respirology Case Reports - 12(2024), 2, Seite n/a-n/a |
Sprache: |
Englisch |
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Beteiligte Personen: |
Eleanor C. Barton [VerfasserIn] |
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Links: |
doi.org [kostenfrei] |
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Themen: |
Chylothorax |
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doi: |
10.1002/rcr2.1303 |
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funding: |
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Förderinstitution / Projekttitel: |
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PPN (Katalog-ID): |
DOAJ097021792 |
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