A chylothorax in a young woman: The difficulties of medical management

Abstract Lymphangioleiomyomatosis is a rare pulmonary disease affecting women of childbearing age. Whilst chylothorax is a well‐recognized complication of the condition, management strategies aren't well‐defined, have low success rates and are often only available at tertiary or specialist centres. We describe a case of a young woman referred to pleural clinic with a chylous effusion found to be secondary to lymphangioleiomyomatosis. Initial medical management was unsuccessful and recurrent drainages caused significant complications. Remission was ultimately achieved with a combination of mTOR inhibitors and interventional radiology techniques..

Medienart:

E-Artikel

Erscheinungsjahr:

2024

Erschienen:

2024

Enthalten in:

Zur Gesamtaufnahme - volume:12

Enthalten in:

Respirology Case Reports - 12(2024), 2, Seite n/a-n/a

Sprache:

Englisch

Beteiligte Personen:

Eleanor C. Barton [VerfasserIn]
Simon Johnson [VerfasserIn]
Neil Collin [VerfasserIn]
Nidhi Bhatt [VerfasserIn]
Nick A. Maskell [VerfasserIn]

Links:

doi.org [kostenfrei]
doaj.org [kostenfrei]
doi.org [kostenfrei]
Journal toc [kostenfrei]

Themen:

Chylothorax
Diseases of the respiratory system
Lymphangiogram
Lymphangioleiomyomatosis
Pleural effusion

doi:

10.1002/rcr2.1303

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

DOAJ097021792