Abnormal Dentition in a Boy with Incontinentia Pigmenti: Case Report
Incontinentia pigmenti (IP) is an X-linked dominant genodermatosis characterized by typical skin lesions along Blaschko’s lines and associated with ocular, dental, nails, hair, skeletal, central nervous system and cardiovascular anomalies. We report a 5-year-old boy with cutaneous hyperpigmentation along Blaschko’s lines, atrophic streaks, strabismus and mental retardation. He showed the characteristic abnormal dentition seen in IP as partial hypodontia, peg-shaped anterior teeth and un-erupted teeth. The expression of IP in boys is exceptional as the disease is lethal in males..
Medienart: |
E-Artikel |
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Erscheinungsjahr: |
2012 |
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Erschienen: |
2012 |
Enthalten in: |
Zur Gesamtaufnahme - volume:9 |
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Enthalten in: |
Journal of Dentistry of Tehran University of Medical Sciences - 9(2012), 3, Seite 267-270 |
Sprache: |
Englisch |
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Beteiligte Personen: |
P Aref [VerfasserIn] |
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Links: |
doaj.org [kostenfrei] |
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PPN (Katalog-ID): |
DOAJ023090928 |
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