Fevers, Sweats, Weight Loss, Oh My! When IgG4 Related Disease Comes Knocking. . 

© The Author(s) 2021..

Immunoglobulin G4-related systemic disease (IgG4-RSD) is a fibro-inflammatory immune condition characterized by IgG4 positive plasma cells, fibrosis, and frequently elevated serum IgG4 level. Akin to sarcoidosis, IgG4-RSD is a systemic disease with diverse organ manifestations linked by common histopathologic features. IgG4-RSD typically presents sub acutely without significant constitutional symptoms or fever. Hepatic Inflammatory pseudotumor (HIP) is a rare manifestation of IgG4-RSD composed of dense lymphoplasmacytic infiltrate and extensive fibrosis. We present an older Asian male who presented with acute onset of fever and weight loss found to have IgG4-RSD complicated by a HIP and concomitant MSSA abscess.

Medienart:

E-Artikel

Erscheinungsjahr:

2021

Erschienen:

2021

Enthalten in:

Zur Gesamtaufnahme - volume:14

Enthalten in:

Clinical medicine insights. Case reports - 14(2021) vom: 12., Seite 11795476211046398

Sprache:

Englisch

Beteiligte Personen:

Essien, Francis [VerfasserIn]
Wolfley, Graey [VerfasserIn]
Tate, Joshua [VerfasserIn]
Carroll, Matthew [VerfasserIn]

Links:

Volltext

Themen:

Autoimmune lymphoproliferative syndrome
Case Reports
Immunoglobulin allotypes
Immunosuppressive agents

Anmerkungen:

Date Revised 05.11.2021

published: Electronic-eCollection

Citation Status PubMed-not-MEDLINE

doi:

10.1177/11795476211046398

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM332712168