Congenital double mitral orifice with severe mitral regurgitation-associated rheumatoid arthritis : a case report

© The Author(s) 2020. Published by Oxford University Press on behalf of the European Society of Cardiology..

BACKGROUND: A double orifice mitral valve (DOMV) represents a rare congenital malformation characterized by two valve orifices with two separate subvalvular apparatus. Double orifice mitral valve is congenital anomaly of the subvalvular mitral valve apparatus consisting of an accessory bridge of fibrous tissue, which partially or completely divides the mitral valve into two orifices.

CASE SUMMARY: A 30-year young male presented with dyspnoea and palpitation for 4 years, joint pain for 2 years and weakness of right upper limb and lower limb for 6 months. On clinical examination, Boutonniere, Swan neck, and Z-deformity of hand and foot metatarsal bone deformities are noted, on further evaluation, patient was diagnosed as a case of DOMV and was managed conservatively since patient was not willing for surgery.

DISCUSSION: Two-dimensional echocardiography is the best detection method, the parasternal short-axis view being most useful to show DOMV.

Medienart:

E-Artikel

Erscheinungsjahr:

2020

Erschienen:

2020

Enthalten in:

Zur Gesamtaufnahme - volume:4

Enthalten in:

European heart journal. Case reports - 4(2020), 4 vom: 11. Aug., Seite 1-4

Sprache:

Englisch

Beteiligte Personen:

Natraj Setty, Huliurdurga Srinivasa Setty [VerfasserIn]
Shankar, Somanna [VerfasserIn]
Yeriswamy, Mogalahally Channabasappa [VerfasserIn]
Manjunath, Cholenahally Nanjappa [VerfasserIn]

Links:

Volltext

Themen:

2D echocardiography
Case Reports
Case report
Double orifice mitral valve
Mitral regurgitation
Rheumatoid arthritis

Anmerkungen:

Date Revised 17.04.2022

published: Electronic-eCollection

Citation Status PubMed-not-MEDLINE

doi:

10.1093/ehjcr/ytaa119

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM31545217X