The Giant Infantile Fibrosarcoma of Fetal Oropharynx and Anterior Neck

Introduction: Infantile fibrosarcoma (IFS) usually arises in the extremities during the first 12 months of life and responds well to surgery. It is unusual in the oropharynx or the prenatal period. Case report: A giant solid mass was first detected in the oropharynx and anterior neck at 24 weeks of gestation by ultrasound and fetal MRI. An EXIT procedure with intrapartum intubation with appropriate supportive therapy was successful. The diagnosis of IFS was made postpartum, and the lesion responded to neoadjuvant chemotherapy. Conclusion: IFS may arise as early as 24 weeks of gestation. In this case, an EXIT procedure allowed postpartum diagnosis with subsequent treatment.

Medienart:

E-Artikel

Erscheinungsjahr:

2022

Erschienen:

2022

Enthalten in:

Zur Gesamtaufnahme - volume:41

Enthalten in:

Fetal and pediatric pathology - 41(2022), 3 vom: 02. Juni, Seite 451-456

Sprache:

Englisch

Beteiligte Personen:

Sıvrıkoz, Tugba Sarac [VerfasserIn]
Uygu, Lutfiye Selcuk [VerfasserIn]
Kunt İşgüder, Çiğdem [VerfasserIn]
Aygun, Erhan [VerfasserIn]
Kalelioglu, Ibrahim Halil [VerfasserIn]
Has, Recep [VerfasserIn]

Links:

Volltext

Themen:

Case Reports
ETV6-NTRK3 gene fusion
Fetal oropharyngeal tumor
Infantile fibrosarcoma
Journal Article
Soft tissue tumor

Anmerkungen:

Date Completed 02.06.2022

Date Revised 02.06.2022

published: Print-Electronic

Citation Status MEDLINE

doi:

10.1080/15513815.2020.1809038

funding:

Förderinstitution / Projekttitel:

PPN (Katalog-ID):

NLM314090169